Recurrent Pulmonary Embolism and Pulmonary Hypertension in a Patient with β-Thalassemia Intermedia
نویسندگان
چکیده
منابع مشابه
Thalassemia Associated Pulmonary Hypertension
Cardiac disease is the main cause of death in both forms of thalassemia; thalassemia major (TM) and thalassemia intermedia (TI). Pulmonary hypertension (PH) is one of the cardiopulmonary morbidities with high mortality that, if not treated, may trigger right-sided heart failure and premature death. PH is defined as a mean pulmonary artery pressure of ≥25 mmHg at rest or ≥30 mmHg during exercise...
متن کاملTreatment with bosentan in a patient with thalassemia intermedia and pulmonary arterial hypertension.
Center for Human Genetics for outstanding cytogenetic and FISH experiments, Dr L. Knoops (Cliniques Universitaires Saint-Luc, Université Catholique de Louvain and Ludwig Institute for Cancer Research, Brussels) for discussions, and Katrien Van Roosbroeck (KU Leuven, Leuven) for providing SEC31A cDNA. They also thank Novartis (Vilvoorde, Belgium) for kindly supplying ruxolitinib. This work was s...
متن کاملTreatment of pulmonary hypertension in three patients with β-thalassemia intermedia using pulmonary arterial hypertension-specific medications
Pulmonary hypertension (PH) is frequent among patients with β-thalassemia intermedia (TI) and β-thalassemia major (TM) (1). Almost 60% of all TI patients develop PH (2). However, no randomized controlled trials have evaluated this condition-specific treatment options. Recent guidelines for the treatment of PH offer no specific recommendations for these patients; moreover, the classification of ...
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Hemophilia A is a bleeding disorder caused by defective production of factor VIII. The main concern associated with the disease is bleeding, especially after trauma and surgeries. Factor VIII replacement therapy is associated with substantial decrease of bleeding events during surgery. However, there have been a number of reports of thromboemblic events in this situ-ation. The present report de...
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A 47-year-old man experienced recurrent pulmonary embolism resistant to aggressive medical and surgical prophylaxis. Although paraneoplastic hypercoagulability was suspected, no endoscopic or radiologic signs of malignancy were detected. Death was the result of electromechanical dissociation, which was attributed to right ventricular outflow obstruction. At autopsy, anaplastic lung carcinoma wa...
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ژورنال
عنوان ژورنال: Journal of Blood & Lymph
سال: 2018
ISSN: 2165-7831
DOI: 10.4172/2165-7831.1000205